Juvenile Paget's Disease with Paranasal Sinus Aplasia
نویسندگان
چکیده
Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
منابع مشابه
Combined Aplasia of Sphenoid, Frontal, and Maxillary Sinuses With Hypoplasia of The Ethmoid Sinus
which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Paranasal sinuses are prone to a great diversity of anomalies. Aplasia of the frontal sinus is a relatively common phenomenon and may be accompanied with hypoplasia of the maxillary sinus, but combined aplasia or underde-velopment of the paranasal sinuses is unusual (1, 2)...
متن کاملTotal aplasia of the paranasal sinuses
Although a variety of theories have been proposed about functions of the paranasal sinuses, not one is clear today. Nonetheless, paranasal sinus-related diseases are associated with a high rate of morbidities. Therefore, it is essential to identify the structure and pathophysiology of the paranasal sinuses. Computed tomography (CT) is a valuable tool displaying anatomic variations and diseases....
متن کاملBilateral Total Aplasia of Paranasal Sinuses : A Rare Case Report
Paranasal sinus anatomical anomalies with unknown etiology are common. Paranasal sinus–related diseases are associated with so high rate of morbidities, it becomes essential to identify the structure and pathophysiology of the paranasal sinuses. Computed tomography (CT) is a valuable tool in displaying its anatomy, any anatomic variations and diseases. As paranasal sinus development is a comple...
متن کاملHigher Body Mass Index and Increased Prevalence of Paranasal Sinus Disease
BACKGROUND We hypothesized that higher body mass index (BMI) was associated with increased prevalence of paranasal sinus disease and examined the hypothesis in Japanese adults. METHODS This was a cross-sectional study including 1350 Japanese adults aged 40 years or more who participated in a health check-up program focusing on brain diseases and metabolic syndrome. Participants were divided i...
متن کاملJuvenile angiofibroma: case report and the role of endoscopic resection.
Juvenile angiofibroma is benign yet aggressive. Due to its inaccessible location in the nasopharynx, open surgery usually requires osteotomies which cause stunting of facial growth in adolescent males. Advances in imaging and treatment techniques have now facilitated more accurate staging of this disease. For small, extracranial tumours limited to the nasal cavity and paranasal sinus, endoscopi...
متن کامل